Atelectasis: An Uncommon Sign of Achalasia in Childhoo

An 11-year-old boy presented to our pediatric pulmonology clinic with a 3-month history of atelectasis evident on his chest radiography. Breath sounds revealed fine crackles in the right lower zone and rhonchi upper zones. His initial pulmonary function test was compatible restrictive disease. Chest tomography that trachea, intermediate, middle lobe bronchi were narrowed by megaesophagus. Esophagogram determined dilatation esophagus “bird-beak” sign esophagogastric junction but it not sufficient diagnose. Esophageal manometry which is gold standard for achalasia performed type 2 diagnosed. symptoms improved following Heller myotomy conducted together Dor fundoplication. Although respiratory problems are more common infants younger children, atypical presentations may also occur during adolescence. Achalasia should be one rare differential diagnoses